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malignant essential hypertension

Pulmonary arterial hypertension associated with portal hypertension (PAH-PH) is a form of pulmonary arterial hypertension (PAH), characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of portal hypertension.

Therapeutic area: Cardiovascular
Rarity: Common
Prevalence: ~1.0M patients globally (est.)
MONDO: MONDO:0001133

Overview

Pulmonary arterial hypertension associated with portal hypertension (PAH-PH) is a form of pulmonary arterial hypertension (PAH), characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of portal hypertension.

Content last reviewed: 2026-06